Cystic fibrosis in children and adults: symptoms and treatment what it is

How to treat cystic fibrosis?

In modern medicine there is a serious inflammation called cystic fibrosis. The disease is characterized as chronic and hard progressive disorder of external secretion and the glands within organs. The disease affects various strata of the population. Unfortunately, the causes of cystic fibrosis to find out pretty hard, and its treatment in most cases is to no avail.

With the progression of the disease is dysfunction of the internal organs, leading to death. However, early detection of symptoms and treatment of cystic fibrosis in adults and children allows you to pause the development of the disease and improve the patient’s quality of life.

What is the disease cystic fibrosis

The very concept cystic fibrosis is borrowed from Latin. Means sticky mucus. Under this term you can think of the disease itself, as in the course of development in patients formed a viscous mucus, which disrupts the organs, tissues and cells.

When you suffer inflammation of the cystic fibrosis bronchi and lungs. With the progression of the disease noted the consequences of the process in the intestinal tract, the stomach and kidneys. Further, the disease progresses into the urinary tract and the ducts of the genital glands.

For reference! Today, there are over five hundred different forms of cystic fibrosis. Each form of the disease occurs with painful symptoms.

Reasons

The reason lies in the cystic fibrosis genetic mutation in the seventh gene. The root cause of such mutations is unknown and scientists are still conducting research on identification of factors of formation of the disease. Today, the experts came to the conclusion that the seventh chromosome is a gene that is responsible for protein synthesis. In the course of a violation of the channel, where the cell membrane of external secretion, where the protein acts as a checkpoint, the accumulation of a large number of chlorine ions.

Due to the annexation of chlorine and protein inside the cell is the attraction of the liquid. It thus produces mucus between the cells. Over time, it becomes viscous and sticky. Losing its function, the mucus becomes a cause of formation of pathological processes in the body.

It is important to note that the eccrine glands are found in every part of the body, but in violation of its functions primarily affect the respiratory system, and then the stomach and liver.

In the stagnation of this material in the lungs and respiratory tract is a violation of cleansing the bronchi from dust, dirt and other small particles that can harm the health. As a result of the process in the human body penetrate the germs and infections that cause the development of many diseases.

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With the development of the inflammatory process due to the accumulation of mucus, dirt and various microorganisms is the disruption of the entire defense system, which greatly affects the immunity of the patient.

During the disorders of the tissues inside the respiratory tract and functions of the cilia, which serve for the cleansing and warming of the inhaled air, is the destruction of bronchi frame. Further the patient has formed a chronic pathology in the respiratory system, which leads to dangerous consequences.

Please note the photos look like healthy lungs and with the defeat of cystic fibrosis:

Symptoms

Symptoms of cystic fibrosis are largely dependent on the patient’s age, lifestyle and the duration of progression of the disease. The signs of the disease in each case may manifest in a special way, but in most cases patients complain of the defeat of the work of the bronchi and gastrointestinal tract.

The disease is characterized by a gradual development of the disease. Symptoms at the initial stage do not appear sharp, so the patient can mix them with infectious disease. Usually in the early stages, patients notice the formation of cough, scratchy throat and frequent sneezing.

In the formation of chronic forms of the disease in patients appearing sputum that accumulates in the upper respiratory tract and bronchi.

The development of cystic fibrosis is quite long and the first symptoms may occur several months after the inflammation.

Other symptoms of inflammation include:

  • small body temperature;
  • cough, accompanied by expectoration;
  • the lack of oxygen;
  • shortness of breath;
  • swelling of the face;
  • dryness of the nasal passages and mouth;
  • the reduction in weight due to the lack of appetite;
  • loss of sleep;
  • the violation of physical development, if the patient became ill in childhood;
  • fatigue;
  • pallor;
  • lethargy;
  • apathy.

It should be noted that the reflex process in the form of cough occurs constantly. Over time it can affect the General condition of the patient, interferes with sleep, disrupts sleep. For prolonged cough in a patient notice the change in color of the skin, swelling of the face.

However, at the initial stage of the disease the symptoms of severe intoxication are not present. But with the development of a chronic form, the patient appears high body temperature, severe coughs, the allocation of thick sputum.

Further the patient starts torturing pain in the head, nausea and vomiting, loss of consciousness.

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To determine the onset of chronic diseases can be due to the change of the shape of the chest. At this time, the patient’s skin becomes dry and inelastic, the hair starts to fall, there is a strong shortness of breath.

Due to the lack of oxygen, the color of the skin changes and becomes bluish tint.

Diagnosis

Before treatment the patient should undergo a diagnostic of cystic fibrosis. To begin with the patient undergoing the study in the laboratory. Accurate diagnosis can after identifying all the symptoms of a chronic process in the bronchi, testing of stool, sputum and blood.

In addition, the patient must undergo a test, which is based on the calculation of the exact amount of chloride ions in the sweat. The analyses can be considered correct only after the introduction of pilocarpine.

When you confirm a larger quantity of chlorides than is permissible, the patient receives a diagnosis of cystic fibrosis. For reliable information, the test should be repeated two more times.

For reference! The content of chlorine exceeds the rate, if rate is higher than 60 mmol/L.

Medication

It should be understood that chronic disease takes long and difficult. To get rid of the inflammation forever is almost impossible, but doctors have to exclude the risk of a rapid process of the disease.

Remember! The treatment of cystic fibrosis should be aimed at reducing signs of inflammation. When remission is necessary to exclude all risks of development of pathology, and during the activation of the disease it is important to take the antibacterial and anti-inflammatory treatment.

It is necessary to determine how and what to treat cystic fibrosis. At the standard course of the disease is assigned to the following exposure methods:

  • Daily cleansing of the nasal passages of accumulated mucus. To handle the nose, you can use the following firstgov: «Phrase», «Marimer», «Humer», «Aqua Maris», «no-Sol», «Dolphin».
  • Take active supplements, vitamin and mineral supplements. They will help to support the immune system of the patient. The patient should not worry and worry, because any stress causes reduced immunity.
  • Impact on inflammation antibiotics will help – «Tarepanda», «Mandal», «Ceftriaxone», «Klacid», «Fromilid UNO.» Drugs with broad spectrum action will help to destroy microorganisms and to improve the condition of the patient. The dosage regimen should be selected with your doctor.
  • In acute processes the patient is prescribed a medication based on hormones. The most popular product from the group of glucocorticosteroids is «Prednisolone». The tool returns the function of the respiratory tract, improves the work of muscles of the bronchi and reduces the inflammatory response.
  • When cystic fibrosis patient, tormented by acute symptoms, the patient should saturate the blood with oxygen.
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An additional treatment will perform physiotherapeutic procedures, inhalations, mud therapy, moxibustion. Effect complex helps to widen blood vessels and improve blood circulation.

Learn how to conduct inhalation here.

Traditional methods

The cystic fibrosis treatment folk remedies is impossible. However, certain recipes can reduce the severity of symptoms and to recover good health of the patient.

For treatment, use the broth to liquefy the phlegm. Tinctures are best prepared on the basis of propolis, thyme, oaks, calendula and chamomile leaves. Drink the decoction every day should be three times a day.

More methods to liquefy phlegm learn here.

In addition, it is useful to the patient inhalation with essential oils and some natural antiseptics. These include sea buckthorn, dandelion, globe-Thistle, vervain, celandine.

To relax muscles and increase patient’s mood, use of lotions with the addition of tincture of wild strawberry, nettle, mother and stepmother, St. John’s wort, Bay leaves.

For cooking gadgets need:

  1. Prepare a decoction of medicinal plants. To do this, boil one liter of water and add the liquid of the selected ingredient.
  2. Allow the infusion to cool to 50 degrees Celsius, and then dip in a mixture of cotton fabric.
  3. Wring the compress and apply to the inflamed area for 15 minutes.
  4. Repeat when the cloth cools down three more times.

Remember! Traditional recipes can be used only as additional therapy, but to use them instead of medical treatment forbidden!

Conclusion

When the diagnosis of cystic fibrosis every day is important to strengthen the immune system. To do this, take vitamins, spend more time outdoors, follow the diet of the patient. Don’t forget to see your doctor regularly and follow all the doctor appointments.